ABERRANT COBALAMIN METABOLISM WITH HOMOCYSTINURIA AND METHYMALONIC ACIDURIA

نویسندگان
چکیده

برای دانلود رایگان متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Maculopathy and retinal degeneration in cobalamin C methylmalonic aciduria and homocystinuria.

1. George F, Brisson C, Poncelet P, et al. Rapid isolation of human endothelial cells from whole blood using S-Endo1 monoclonal antibody coupled with immunomagnetic beads: demonstration of endothelial injury after angioplasty. Thromb Haemost. 1992;67:147-153. 2. Rambaud JC, Galian A, Touchard G, et al. Digestive tract and renal small vessel hyalinosis, idiopathic nonarteriosclerotic intracerebr...

متن کامل

Abnormal Deoxyuridine Suppression Test in Congenital Methylmalonic Aciduria-Homocystinuria Without Megaloblastic Anemia: Divergent Biochemical and Morphological Bone Marrow Manifestations of Disordered Cobalamin Metabolism in Man

We studied two brothers (J.R. and M.R.) with the cobalamin D variant of congenital methylmalonic aciduria-homocystinuria. whose previously reported lack of megaloblastic anemia conflicted with current concepts of cobalamin’s role in DNA synthesis and the “methyltetrahydrofolate (MTHF) trapS’ hypothesis. Both subjects were indeed hematologically normal. although JR. had a mean corpuscular volume...

متن کامل

Abnormal Deoxyuridine Suppression Test in Congenital Methylmalonic Aciduria-Homocystinuria Without Megaloblastic Anemia: Divergent Biochemical and Morphological Bone Marrow Manifestations of Disordered Cobalamin Metabolism in Man

We studied two brothers (J.R. and M.R.) with the cobalamin D variant of congenital methylmalonic aciduria-homocystinuria. whose previously reported lack of megaloblastic anemia conflicted with current concepts of cobalamin’s role in DNA synthesis and the “methyltetrahydrofolate (MTHF) trapS’ hypothesis. Both subjects were indeed hematologically normal. although JR. had a mean corpuscular volume...

متن کامل

cobalamin metabolism in man biochemical and morphological bone marrow manifestations of disordered aciduria-homocystinuria without megaloblastic anemia: divergent Abnormal deoxyuridine suppression test in congenital methylmalonic

http://bloodjournal.hematologylibrary.org/site/misc/rights.xhtml#repub_requests Information about reproducing this article in parts or in its entirety may be found online at: http://bloodjournal.hematologylibrary.org/site/misc/rights.xhtml#reprints Information about ordering reprints may be found online at: http://bloodjournal.hematologylibrary.org/site/subscriptions/index.xhtml Information abo...

متن کامل

Abnormal Deoxyuridine Suppression Test in Congenital Methylmalonic Aciduria-Homocystinuria Without Megaloblastic Anemia: Divergent Biochemical and Morphological Bone Marrow Manifestations of Disordered Cobalamin Metabolism in Man

We studied two brothers (J.R. and M.R.) with the cobalamin D variant of congenital methylmalonic aciduria-homocystinuria. whose previously reported lack of megaloblastic anemia conflicted with current concepts of cobalamin’s role in DNA synthesis and the “methyltetrahydrofolate (MTHF) trapS’ hypothesis. Both subjects were indeed hematologically normal. although JR. had a mean corpuscular volume...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

ژورنال

عنوان ژورنال: Pediatric Research

سال: 1984

ISSN: 0031-3998,1530-0447

DOI: 10.1203/00006450-198404001-00780